In recent years there have been huge advances in the understanding of
the genetic and molecular basis of the fibrocystic diseases. This volume
provides a thorough review of fibrocyctic diseases that affect the
liver. It contains in-depth discussions of the genetics, molecular
biology, pathogenesis, histology, clinical presentations, complications
of, treatment, and prognosis of the conditions affecting children and
adults, and hence will be the gold-standard reference for these
conditions. In addition, the histological features that distinguish
these conditions from other potentially fibrosing hepatopathies are
illustrated. Conditions with syndromic features involving the kidney or
other organ systems are also reviewed. Thorough review of the clinical
phenotypes, their presentations, treatment, potential complications of,
and prognosis is discussed.
Fibrocystic Diseases of the Liver will be an invaluable resource for
hepatologists, gastroenterologists, nephrologists, and hepatic surgeons
who care for children and adults with liver disease, as well as basic
scientists in molecular genetics, hepatobiliary pathophysiology,
hepatology and nephrology.